BRUGADA SYNDROME

brugada channelopathy

• Brugada syndrome is an inherited disorder in which cardiac sodium ion channels are malfunctional.
• On ECG, there are ST elevation and incomplete or complete right bundle branch block in leads V1-3.
• There are 2 main types:
   Type 1 (typical): has “coved” pattern
   Type 2: has “saddle-back” pattern
• Brugada syndrome is associated with an increased risk of ventricular arrhythmias.

brugada type 1
brugada type 1

brugada type 2
brugada type 2

related topics




long qt syndrome
bundle branch block
polymorphic vt
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